Wednesday, April 18, 2012

Red Scaly Baby Syndrome (Leiner's Disease)

RSB is a tragic entity which is a result of severe immunodeficiency.  Usually C5 deficient, these patients can also be C3 deficient as well as have other immunodeficiencies.  They display severe rashes that look like seb derm, and they often suffer from infections from Gram negatives and yeast.  This disease is usually fatal, but success has been reported with bone marrow transplant.  I gave you all the clues because it is such a good picture of such a rare disease, I thought you should see it and know about it.
Dr. B

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